A Rare Case of Pulmonary Leiomyosarcoma

Authors

  • Jialin He Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Yun Tang Department of Geriatric, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Fei Zhao Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Bo Zheng Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Shihai Tang Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Juan Gong Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Li Wang Department of Geriatric, People’s Hospital of Leshan, Leshan, Sichuan Province, China
  • Yang Zhou Department of Cardiothoracic Surgery, People’s Hospital of Leshan, Leshan, Sichuan Province, China

Keywords:

Pulmonary leiomyosarcoma, Pulmonary embolism, Diagnosis

Abstract

Leiomyosarcoma commonly occurs in the abdomen, retroperitoneum, large blood vessels, and uterus[1]. Cardiac leiomyosarcoma is a rare and highly aggressive sarcoma. We reported a case of a 63-year-old male with pulmonary artery leiomyosarcoma. Transthoracic echocardiography showed a large 4.4×2.3 cm hypoechoic mass in the right ventricular outflow tract and pulmonary artery. Computed tomography pulmonary angiography showed a filling defect in a similar location. The initial impression was PE, but a tumor was not ruled out. An emergency surgery was performed due to progressively worse chest distress and dyspnea. A yellow mass that had adhered to the ventricular septum and pulmonary artery wall was detected to be compressing the pulmonary valve. Immunohistochemistry confirmed tumor cells positive staining for Desmin and smooth muscle actin and negative staining for S-100, CD34, myogenin, or myoglobin, and KI67(+)80%, indicating leiomyosarcoma. Pulmonary leiomyosarcoma showed a side-inserted heart chamber filling defect in CTA and should be excised when the patient suddenly deteriorated.

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Published

2023-03-31

How to Cite

He, J., Tang, Y., Zhao, F., Zheng, B., Tang, S., Gong, J., Wang, L., & Zhou, Y. (2023). A Rare Case of Pulmonary Leiomyosarcoma. Acta Medica Indonesiana, 55(1), 83. Retrieved from https://actamedindones.org/index.php/ijim/article/view/1898

Issue

Vol. 55 No. 1 (2023): Acta Medica Indonesiana

Section

CASE REPORT

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