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  2. Vol 51, No 2 (2019)
  3. Saveria

An 18-Year-Old Man with Idiopathic Non-cirrhotic Portal Hypertension

Irene Saveria, Syifa Mustika

Abstract


Non-Cirrhotic Portal Hypertension (NCPH) is a rare cause of hematemesis and melena. Like in cirrhotic patient, hematemesis in NCPH patient was caused by rupture of esophageal varices. But unlike in cirrhotic patient, in NCPH there are no sign of liver failure, because liver physiology is still normal. We reported case of male patient with NCPH that had hematemesis because of rupture of esophageal varices.


Keywords


non-cirrhotic portal hypertension; hematemesis; rupture variceal esophagus

References


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Goel A, Elias JE, Eapen CE, et al. Idiopathic non-cirrhotic intrahepatic portal hypertension (NCIPH) - Newer insights into pathogenesis and emerging newer treatment options. J Clin Exp Hepatol. 2014; 4(3): 247–256.

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